Arrhythmogenic right ventricular cardiomyopathy is a disease that affects mainly the right ventricle. It causes the replacement of heart muscle tissue with adipose tissue, with consequent structural abnormalities. It manifested by arrhythmias and worsening dysfunction, ranging from palpitations to syncope. If not treated in time, it causes arrhythmias which can lead to death within minutes.
In 30-50% of cases have a family distribution and is transmitted either by dominant genes recessive. For this reason, the family history items are a fundamental diagnostic criterion. In addition to history, the diagnosis includes ECG graphs, ECG and MRI. To assess the functioning of the ventricle, you may also use an electrophysiological study. This allows you to determine the type of arrhythmia and when it can be tolerated by the body.
Current treatments are used primarily to prevent arrhythmias. The first step is to eliminate the significant physical activity, which could be fatal. That's why in the past the arrhythmogenic right ventricle has claimed many victims among sportsmen. You also need to proceed with a pharmacological therapy with beta-blockers, amiodarone, sotalol. In case of arrhythmias can not be controlled in a traditional manner, it can be useful to proceed with surgical interventions aimed at blocking arrhythmias in the bud. For patients who have already suffered a heart attack, you may also need the implantation of a defibrillator.